A rare case of McCune Albright syndrome

Authors

  • Pooja Patil Department of Obstetrics and Gynecology, LN Medical College, JK Hospital and Medical Research Centre, Bhopal, Madhya Pradesh, India
  • Siftie-Kaur Banga Department of Obstetrics and Gynecology, LN Medical College, JK Hospital and Medical Research Centre, Bhopal, Madhya Pradesh, India

DOI:

https://doi.org/10.18203/2320-1770.ijrcog20191979

Keywords:

McCune Albright, Precocious puberty

Abstract

McCune Albright syndrome is characterized by the clinical triad of precocious puberty, polyostotic fibrous dysplasia, and café-au-lait pigmentation. Authors reported the case of a 6 years old girl presenting with vaginal bleeding. Investigations showed high serum oestrogen levels, with low FSH and LH levels. Ultrasonography revealed a multiloculated right ovarian cyst. Based on the history and investigations, the patient was diagnosed as a case of precocious puberty. In order to rule out the presence of any ovarian malignancy, tumour markers were sent and found to be within the normal range. A CT pelvis was done which revealed fibrous dysplasia of the pelvic bone. The coexistence of precocious puberty with fibrous dysplasia confirmed the diagnosis of McCune Albright syndrome.

References

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Published

2019-04-29

Issue

Section

Case Reports