Youssef’s Syndrome - a complication of corrective surgery for mullerian anomaly

Authors

  • Vineet Mishra Department of Obstetrics and Gynaecology, Institute of Kidney Disease and Research Centre, Ahmadabad, Gujarat, India
  • Suwa Saini Department of Obstetrics and Gynaecology, SP Medical College, Bikaner, Rajasthan, India
  • Rohina Aggarwal Department of Obstetrics and Gynaecology, Institute of Kidney Disease and Research Centre, Ahmadabad, Gujarat, India
  • Priyankur Roy Department of Obstetrics and Gynaecology, Institute of Kidney Disease and Research Centre, Ahmadabad, Gujarat, India
  • Shaheen Hokabaj Department of Obstetrics and Gynaecology, Institute of Kidney Disease and Research Centre, Ahmadabad, Gujarat, India

DOI:

https://doi.org/10.18203/2320-1770.ijrcog20163900

Keywords:

Cervicovaginal agenesis, Hysterectomy, Vaginoplasty, Youssef’s Syndrome

Abstract

The presence of cervicovaginal agenesis with unicornuate uterus is a very rare mullerian anomaly. Presence of functioning unicornuate uterus poses as a great challenge for gynecologist, because a successful repair could restore normal menses and may preserve the patient’s fertility. Though, a complication of this surgery (utero-vaginal anastomosis) is Youssef’s Syndrome. We, hereby report a case of 16 year old unmarried female with complete cervicovaginal agenesis with unicornuate uterus, who initially underwent vaginoplasty (McIndoe’s) along with uterovaginal anastomosis in order to preserve her uterus, but subsequently required hysterectomy due to Youssef’s Syndrome.

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Published

2016-12-14

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Section

Case Reports