A challenging case of SLE associated with intrahepatic cholestasis and atypical Wilson's disease

Authors

  • Jyoti Kankanala Department of Obstetrics and Gynecology, Citizens Hospital, Hyderabad, Telangana, India

DOI:

https://doi.org/10.18203/2320-1770.ijrcog20172381

Keywords:

Autoimmune diseases, Cholestasis, SLE, Wilson's disease

Abstract

We herewith present a case of SLE which reflects that appropriate Multidisciplinary approach gives good outcome inspite of risk factors including prematurity. Systemic lupus erythematosus (SLE) an autoimmune disease in itself a high-risk factor along with intrahepatic cholestasis and atypical wilson's disease it’s a tough journey for clinicians as well as the family but good timely intervention by appriopriate investigations gave an excellent outcome. Emergency LSCS was performed for pathological CTG at 31 weeks, mother and child followed up for a year and a half then we are reporting this case.

References

Mills JA. Systemic Lupus Erythematosus. N Engl J Med. 1994;330:1871.

Lateef A, Petri M. Management of pregnancy in systemic lupus erythematosus. Nat Rev Rheumatol. 2012;8(12):710-8

Ostensen M, Khamashta M, Lockshin M, Parke A, Brucato A, Carp H, et al. Anti-inflammatory and immunosuppressivedrugs and reproduction. Arthritis Res Ther. 2006;8(3):209

Del Ross T, Ruffatti A, Visentin MS, Tonello M, Calligaro A, Favaro M, et al. Treatment of 139 pregnancies in antiphospholipid positive women not fulfilling criteria for antiphospholipid syndrome: a retrospective study. J Rheumatol. 2013;40(4):425-9.

Petri M, Qazi U. Management of antiphospholipid syndrome in pregnancy. Rheum Dis Clin North Am. 2006;32(3):591-607.

Hayslett JP, Lynn RI. Effect of pregnancy in patients with lupus nephropathy. Kidney Int 1980;18:207-20.

Buyon JP, Rupel A, Clancy RM. Neonatal lupus syndromes. Lupus 2004;13:705-12.

Lee LA. The clinical spectrum of neonatal lupus. Arch Dermatol Res. 2009;301:107-10.

Silverman E, Jaeggi E. Non-cardiac manifestations of neonatal lupus erythematosus. Scand J Immunol. 2010;72:223-5

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Published

2017-05-25

Issue

Section

Case Reports